Compound Name
|
Diease
|
| Lactic acid-2TMS |
Methylmalonic Acidemia |
| ۲-Hydroxyisobutyric acid-2TMS |
Propionic Acidemia |
| Caproic acid-TMS |
۳-Ketothiolase Deficiency |
| Glycolic acid-2TMS |
Isovaleric Acidemia |
| Glyoxylic acid-oxime-2TMS |
۳-Methylcrotonyl-CoA Carboxylase Deficiency |
| Oxalic acid-2TMS |
Multiple Carboxylase Deficiency |
| ۲-Hydroxybutyric acid-2TMS |
۳-OH-3-Methylglutaric Aciduria |
| ۳-Hydroxypropionic acid-2TMS |
۳-Methylglutaconic Aciduria |
| Pyruvic acid-oxime-2TMS |
Glutaric Aciduria Type I |
| Valproic acid-TMS |
Glutaric Aciduria Type II ? |
| ۳-Hydroxybutyric acid-2TMS |
۳-OH-Isobutyric Aciduria ? |
| ۳-Hydroxyisobutyric acid-2TMS |
۵-Oxoprolinuria ? |
| ۲-Hydroxyisovaleric acid-2TMS |
۲-Hydroxyglutaric Acidemia ? |
| ۲-Methyl-3-hydroxybutyric acid-2TMS |
۴-Hydroxybutyric Aciduria |
| Malonic acid-2TMS |
Mevalonic Aciduria |
| ۳-Hydroxyisovaleric acid-2TMS |
Glyceroluria ? |
| ۲-Keto-isovaleric acid-oxime-2TMS |
Primary Hyperoxaluria Type I ? |
| Methylmalonic acid-2TMS |
L-Glyceric Acidemia ?
(Primary Hyperoxaluria Type II ? ) |
| ۲-ethyl-3-OH-propionic-2TMS |
۲-Ketoadipic Aciduria ? |
| Urea-2TMS |
Alcaptunuria |
| ۴-Hydroxybutyric acid-2TMS |
Urea Cycle Disorder ? / OTC Deficiency? |
| ۲-Hydroxyisocaproic acid-2TMS |
Phenylketonuria |
| ۳-Hydroxyvaleric acid-2TMS |
Maple Syrup Urine Disease |
| Acetoacetic acid-2TMS |
Tyrosinemia Type I |
| ۲-Hydroxy-3-Methylvaleric acid-2TMS |
MCAD Deficiency? |
| Benzoic acid-TMS |
Canavan Disease |
| Acetoacetic acid-oxime-2TMS |
Lactic Aciduria (Condition) |
| Octanoic acid-TMS |
Respiratory chain disease |
| ۲-keto-3-methylvaleric-ox-2 |
Ketosis (Condition) |
| ۲-Methyl-3-hydroxyvaleric acid-2TMS |
Dicarboxylic Aciduria |
| Glycerol-3TMS |
Ketotic dicarboxylic aciduria? |
| Phosphoric acid-3TMS |
Non-ketotic dicarboxylic aciduria? |
| Acetylglycine-TMS |
۳-Hydroxydicarboxylic Aciduria (Condition) |
| Ethylmalonic acid-2TMS |
Zellweger Syndrome |
| ۲-Methyl-3-hydroxyvaleric acid-2TMS(2) |
Metabloic disorders of purine and pyrimidine |
| ۲-Ketoisocaproic acid-oxime-2TMS |
Valproic acid treatment? |
| Phenylacetic acid-TMS |
Ethosuccimide treatment? |
| Maleic acid-2TMS |
Glycerol treatment ? |
| Succinic acid-2TMS |
Carbocysteine administration? |
| Methylsuccinic acid-TMS |
Aspirin administration? |
| Glyceric acid-3TMS |
Sodium benzoate administration? |
| Fumaric acid-2TMS |
MCT milk feeding? |
| Uracil-2TMS |
Food containing vanilla taking? |
| Propionylglycine-TMS |
Special fomula containing vanilla feeding |
| Acetylglycine-2TMS |
Ascorbic acid infusion? |
| Mevalonolactone-TMS |
Neonatal transient hypertyrosinemia? |
| mevalonolactone-origin fragment |
Severe liver dysfunction? |
| Isobutyrylglycine-TMS |
Hypoxia? |
| ۲-propyl-3-hydroxy-pentanoic acid-2TMS |
Acetonemic vomiting? |
| Mesaconic acid-2TMS |
Neuroblastoma? |
| Glutaric acid-2TMS |
|
| ۳-Methylglutaconic acid-2TMS |
|
| ۳-Methylglutaric acid-2TMS |
|
| ۲-Propyl-3-ketopentanoic acid-2TMS |
|
| Propionylglycine-2TMS |
|
| Isobutyrylglycine-2TMS |
|
| ۲-Deoxytetronic acid-3TMS |
|
| Butyrylglycine-TMS |
|
| ۳-Methylglutaconic acid(E)-2TMS |
|
| Glutaconic acid-2TMS |
|
| succinylacetone-ox-origine fragment |
|
| decanoic-1 |
|
| ۲-Propyl-5-OH-pentanoic(VPA)-2 |
|
| ۳-methylglutaconic-2(3) |
|
| isovalerylglycine-1 |
|
| Butyrylglycine-2TMS |
|
| Malic acid-3TMS |
|
| Adipic acid-2TMS |
|
| Phenyllactic acid-2TMS |
|
| Isovalerylglycine-2TMS |
|
| ۲-Hexenedioic acid-2TMS |
|
| ۵-Oxoproline-2TMS |
|
| Thiodiglycolic acid-2TMS |
|
| ۳-Methyladipic acid-2TMS |
|
| ۲-Propyl-glutaric acid-2TMS |
|
| ۷-Hydroxoctanoic acid-2TMS |
|
| ۵-Hydroxy-2-furoic acid-2TMS |
|
| Tiglylglycine-2TMS |
|
| ۳-Methylcrotonoylglycine-TMS |
|
| Tiglylglycine-TMS |
|
| ۳-Methylcrotonoylglycine-2TMS |
|
| ۳-Hydroxyglutaric acid-3TMS |
|
| ۲-Hydroxyglutaric acid-3TMS |
|
| Pimelic acid-2TMS |
|
| ۳-Hydroxy-3-methylglutaric acid-3TMS |
|
| ۳-Hydroxyphenylacetic acid-2TMS |
|
| ۴-Hydroxybenzoic acid-2TMS |
|
| ۲-Ketoglutaric acid-oxime-3TMS |
|
| ۴-Hydroxyphenylacetic acid-2TMS |
|
| ۲-Ketoglutaric acid-oxime-3TMS |
|
| Hexanoylglycine-2TMS |
|
| Phenylpyruvic acid-oxime-2TMS |
|
| N-Acetylaspartic acid-2TMS |
|
| ۲-Hydroxyadipic acid-3TMS |
|
| Octenedioic acid-2TMS |
|
| ۳-Hydroxyadipic acid-3TMS |
|
| Suberic acid-2TMS |
|
| ۳-Methylglutaconic acid-2TMS |
|
| ۲-Keto-adipic-OX-3 |
|
| Aconitic acid-3TMS |
|
| Orotic acid-3TMS |
|
| Vanillic-2 (3-Methoxy-4-hydroxybenzoic acid-2TMS) |
|
| Homovanillic acid-2TMS |
|
| Azelaic acid-2TMS |
|
| Hippuric acid-2TMS |
|
| Isocitric acid-4TMS |
|
| Citric acid-4TMS |
|
| Hippuric acid-TMS |
|
| Homogentisic acid-3TMS |
|
| Methylcitric acid-4TMS |
|
| ۳-(۳-Hydroxyphenyl)-3-hydroxypropionic acid-3TMS |
|
| Methylcitric acid-4TMS |
|
| ۳-Hydroxyoctenedioic acid-3TMS |
|
| ۳-Hydroxysuberic acid-3TMS |
|
| Vanilmandelic acid-3TMS |
|
| Sebacic acid-2TMS |
|
| Decadienedioic acid-2TMS |
|
| ۴-Hydroxyphenyllactic acid-3TMS |
|
| ۴-Hydroxyphenylpyruvic acid-oxime-2TMS |
|
| ۲-Hydroxyhippuric acid-3TMS |
|
| ۳-Indoleacetic acid |
|
| Palmitic acid TMS |
|
| ۲-Hydroxysebacic acid -3TMS |
|
| ۳-Hydroxysebacic acid -3TMS |
|
| ۲-Hydroxyhippuric acid-2TMS |
|
| Dodecanedioic acid-2TMS |
|
| N-Acetyltyrosine-3TMS |
|
| Uric acid-4TMS |
|
| ۳,۶-Epoxydodecanedioic acid-2TMS |
|
| Suberylglycine-2TMS |
|
| ۳-hydroxydodecanedioic acid-3TMS |
|
| ۳,۶-Epoxytetradecanedioic acid-2TMS |
|